Fucosidase Alpha L1, Tissue (FUCa1)
A-FU; aFU; Alpha-L-Fucosidase; Alpha-L-fucoside fucohydrolase 1
This enzyme is also called alpha-fucosidase. This enzyme participates in n-glycan degradation and glycan structures - degradation.
Alpha-Fucosidase is an enzyme that breaks down fucose.Fucosidosis is an autosomal recessive lysosomal storage disease caused by defective alpha-L-fucosidase with accumulation of fucose in the tissues. Different phenotypes include clinical features such as neurologic deterioration, growth retardation, visceromegaly, and seizures in a severe early form; coarse facial features, angiokeratoma corporis diffusum, spasticity and delayed psychomotor development in a longer surviving form; and an unusual spondylometaphyseoepiphyseal dysplasia in yet another form.
Organism species: Homo sapiens (Human)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Hu01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Hu01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Hu01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Hu01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Hu01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Mus musculus (Mouse)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Mu01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Mu01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Mu01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Mu01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Mu01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Rattus norvegicus (Rat)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Ra01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Ra01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Ra01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Ra01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Ra01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Canis familiaris; Canine (Dog)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Ca01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Ca01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Ca01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Ca01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Ca01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Sus scrofa; Porcine (Pig)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Po01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Po01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Po01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Po01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Po01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Bos taurus; Bovine (Cattle)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Bo01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Bo01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Bo01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Bo01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Bo01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Oryctolagus cuniculus (Rabbit)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Rb01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Rb01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Rb01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Rb01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Rb01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Rhesus monkey (Simian)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPW005Mo01 | Recombinant Fucosidase Alpha L1, Tissue (FUCa1) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAW005Mo01 | Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IP. |
| PAW005Mo01 | Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) | WB; IHC; ICC; IF. | |
| Assay Kits | CLW005Mo01 | CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | CLIA assay for Antigen Detection |
| ELW005Mo01 | ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) | Enzyme-linked immunosorbent assay for Antigen Detection |
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