Aspartylglucosaminidase (AGA)
AGU; ASRG; GA; N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase; Glycosylasparaginase; N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase
Aspartylglucosaminidase is an amidohydrolase enyzme involved in the catabolism of N-linked oligosaccharides of glycoproteins. It cleaves asparagine from N-acetylglucosamines as one of the final steps in the lysosomal breakdown of glycoproteins. The lysosomal storage disease aspartylglycosaminuria is caused by a deficiency in the AGA enzyme.
Defects in AGA are the cause of aspartylglucosaminuria (AGU) . AGU is an inborn lysosomal storage disease. Clinical features of AGU include mild to severe mental retardation manifesting from the age of 2, coarse facial features and mild connective tissue abnormalities. This recessively inherited disease is overrepresented in the Finnish population.
Organism species: Homo sapiens (Human)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Hu01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Hu01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Hu01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Hu01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Hu01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Mus musculus (Mouse)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Mu01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Mu01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Mu01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Mu01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Mu01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Rattus norvegicus (Rat)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Ra01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Ra01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Ra01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Ra01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Ra01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Canis familiaris; Canine (Dog)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Ca01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Ca01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Ca01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Ca01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Ca01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Sus scrofa; Porcine (Pig)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Po01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Po01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Po01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Po01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Po01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Bos taurus; Bovine (Cattle)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Bo01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Bo01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Bo01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Bo01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Bo01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Oryctolagus cuniculus (Rabbit)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Rb01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Rb01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Rb01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Rb01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Rb01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Rhesus monkey (Simian)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU525Mo01 | Recombinant Aspartylglucosaminidase (AGA) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU525Mo01 | Monoclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IP. |
| PAU525Mo01 | Polyclonal Antibody to Aspartylglucosaminidase (AGA) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU525Mo01 | CLIA Kit for Aspartylglucosaminidase (AGA) | CLIA assay for Antigen Detection |
| ELU525Mo01 | ELISA Kit for Aspartylglucosaminidase (AGA) | Enzyme-linked immunosorbent assay for Antigen Detection |
Reference
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Erratum
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