Dystonin (DST)
BP240; BPA; BPAG1; CATX-15; DMH; MACF2; Dystonia musculorum protein; Bullous Pemphigoid Antigen 1; Hemidesmosomal plaque protein; 230 kDa bullous pemphigoid antigen
Organism species: Homo sapiens (Human)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Hu01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Hu01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Hu01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Hu01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Hu01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Mus musculus (Mouse)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Mu01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Mu01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Mu01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Mu01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Mu01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Rattus norvegicus (Rat)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Ra01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Ra01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Ra01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Ra01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Ra01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Canis familiaris; Canine (Dog)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Ca01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Ca01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Ca01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Ca01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Ca01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Sus scrofa; Porcine (Pig)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Po01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Po01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Po01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Po01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Po01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Bos taurus; Bovine (Cattle)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Bo01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Bo01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Bo01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Bo01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Bo01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Oryctolagus cuniculus (Rabbit)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Rb01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Rb01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Rb01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Rb01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Rb01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Organism species: Rhesus monkey (Simian)
| PRODUCT TYPE | CATALOG NO. | PRODUCT NAME | APPLICATIONS |
|---|---|---|---|
| Proteins | RPU401Mo01 | Recombinant Dystonin (DST) | Positive Control; Immunogen; SDS-PAGE; WB. |
| Antibodies | MAU401Mo01 | Monoclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IP. |
| PAU401Mo01 | Polyclonal Antibody to Dystonin (DST) | WB; IHC; ICC; IF. | |
| Assay Kits | CLU401Mo01 | CLIA Kit for Dystonin (DST) | CLIA assay for Antigen Detection |
| ELU401Mo01 | ELISA Kit for Dystonin (DST) | Enzyme-linked immunosorbent assay for Antigen Detection |
Reference
"Human bullous pemphigoid antigen (BPAG1). Amino acid sequences deduced from cloned cDNAs predict biologically important peptide segments and protein domains."
J. Biol. Chem. 266:17784-17790(1991) [PubMed] [Europe PMC] [Abstract]
"Cloning of the 5' mRNA for the 230-kD bullous pemphigoid antigen by rapid amplification of cDNA ends."
J. Invest. Dermatol. 101:244-246(1993) [PubMed] [Europe PMC] [Abstract]
"Novel alternative splicings of BPAG1 (bullous pemphigoid antigen 1) including the domain structure closely related to MACF (microtubule actin cross-linking factor)."
J. Biol. Chem. 277:6682-6687(2002) [PubMed] [Europe PMC] [Abstract]
"Complete sequencing and characterization of 21,243 full-length human cDNAs."
Nat. Genet. 36:40-45(2004) [PubMed] [Europe PMC] [Abstract]
"The DNA sequence and analysis of human chromosome 6."
Nature 425:805-811(2003) [PubMed] [Europe PMC] [Abstract]
"Cloning and characterization of the neural isoforms of human dystonin."
Genomics 29:777-780(1995) [PubMed] [Europe PMC] [Abstract]
"Integrators of the cytoskeleton that stabilize microtubules."
Cell 98:229-238(1999) [PubMed] [Europe PMC] [Abstract]
"Comparison of molecularly cloned bullous pemphigoid antigen to desmoplakin I confirms that they define a new family of cell adhesion junction plaque proteins."
J. Biol. Chem. 266:12555-12559(1991) [PubMed] [Europe PMC] [Abstract]
"The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC)."
Genome Res. 14:2121-2127(2004) [PubMed] [Europe PMC] [Abstract]
"Prediction of the coding sequences of unidentified human genes. XI. The complete sequences of 100 new cDNA clones from brain which code for large proteins in vitro."
DNA Res. 5:277-286(1998) [PubMed] [Europe PMC] [Abstract]
"Construction of expression-ready cDNA clones for KIAA genes: manual curation of 330 KIAA cDNA clones."
DNA Res. 9:99-106(2002) [PubMed] [Europe PMC] [Abstract]
"Isolation of complementary DNA for bullous pemphigoid antigen by use of patients' autoantibodies."
J. Clin. Invest. 82:1864-1870(1988) [PubMed] [Europe PMC] [Abstract]
"The hemidesmosomal plaque. I. Characterization of a major constituent protein as a differentiation marker for certain forms of epithelia."
Differentiation 45:207-220(1990) [PubMed] [Europe PMC] [Abstract]
"Identification of a second protein product of the gene encoding a human epidermal autoantigen."
Biochem. J. 300:851-857(1994) [PubMed] [Europe PMC] [Abstract]
"An essential cytoskeletal linker protein connecting actin microfilaments to intermediate filaments."
Cell 86:655-665(1996) [PubMed] [Europe PMC] [Abstract]
"The N terminus of the transmembrane protein BP180 interacts with the N-terminal domain of BP230, thereby mediating keratin cytoskeleton anchorage to the cell surface at the site of the hemidesmosome."
Mol. Biol. Cell 11:277-286(2000) [PubMed] [Europe PMC] [Abstract]
"Structural analysis of the predicted coiled-coil rod domain of the cytoplasmic bullous pemphigoid antigen (BPAG1). Empirical localization of the N-terminal globular domain-rod boundary."
J. Biol. Chem. 271:9716-9722(1996) [PubMed] [Europe PMC] [Abstract]
"The hemidesmosomal protein bullous pemphigoid antigen 1 and the integrin beta 4 subunit bind to ERBIN. Molecular cloning of multiple alternative splice variants of ERBIN and analysis of their tissue expression."
J. Biol. Chem. 276:32427-32436(2001) [PubMed] [Europe PMC] [Abstract]
"Analysis of the interactions between BP180, BP230, plectin and the integrin alpha6beta4 important for hemidesmosome assembly."
J. Cell Sci. 116:387-399(2003) [PubMed] [Europe PMC] [Abstract]
"Interaction of the bullous pemphigoid antigen 1 (BP230) and desmoplakin with intermediate filaments is mediated by distinct sequences within their COOH terminus."
Mol. Biol. Cell 14:1978-1992(2003) [PubMed] [Europe PMC] [Abstract]
"A quantitative atlas of mitotic phosphorylation."
Proc. Natl. Acad. Sci. U.S.A. 105:10762-10767(2008) [PubMed] [Europe PMC] [Abstract]
"BPAG1e maintains keratinocyte polarity through beta4 integrin-mediated modulation of Rac1 and cofilin activities."
Mol. Biol. Cell 20:2954-2962(2009) [PubMed] [Europe PMC] [Abstract]
"BPAG1 isoform-b: complex distribution pattern in striated and heart muscle and association with plectin and alpha-actinin."
Exp. Cell Res. 316:297-313(2010) [PubMed] [Europe PMC] [Abstract]
"A homozygous nonsense mutation within the dystonin gene coding for the coiled-coil domain of the epithelial isoform of BPAG1 underlies a new subtype of autosomal recessive epidermolysis bullosa simplex."
J. Invest. Dermatol. 130:1551-1557(2010) [PubMed] [Europe PMC] [Abstract]
"Initial characterization of the human central proteome."
BMC Syst. Biol. 5:17-17(2011) [PubMed] [Europe PMC] [Abstract]
"System-wide temporal characterization of the proteome and phosphoproteome of human embryonic stem cell differentiation."
Sci. Signal. 4:RS3-RS3(2011) [PubMed] [Europe PMC] [Abstract]
"Hereditary sensory autonomic neuropathy caused by a mutation in dystonin."
Ann. Neurol. 71:569-572(2012) [PubMed] [Europe PMC] [Abstract]
"Autosomal recessive epidermolysis bullosa simplex due to loss of BPAG1-e expression."
J. Invest. Dermatol. 132:742-744(2012) [PubMed] [Europe PMC] [Abstract]
"Identification of IGPR-1 as a novel adhesion molecule involved in angiogenesis."
Mol. Biol. Cell 23:1646-1656(2012) [PubMed] [Europe PMC] [Abstract]
"An enzyme assisted RP-RPLC approach for in-depth analysis of human liver phosphoproteome."
J. Proteomics 96:253-262(2014) [PubMed] [Europe PMC] [Abstract]
"An EB1-binding motif acts as a microtubule tip localization signal."
Cell 138:366-376(2009) [PubMed] [Europe PMC] [Abstract]