Call Now

Coenzyme Q6 Homolog, Monooxygenase (COQ6)

CGI-10; Coenzyme Q10 monooxygenase 6; Ubiquinone biosynthesis monooxygenase COQ6, mitochondrial

Coenzyme Q (Q) is a lipid that functions as an electron carrier in the mitochondrial respiratory chain in eukaryotes. Coq6 mutants are unable to grow on nonfermentable carbon sources and do not synthesize Q but instead accumulate the Q biosynthetic intermediate 3-hexaprenyl-4-hydroxybenzoic acid. The Coq6 polypeptide is imported into the mitochondria in a membrane potential-dependent manner. Coq6p is a peripheral membrane protein that localizes to the matrix side of the inner mitochondrial membrane. COQ6 encodes a flavin-dependent monooxygenase required for one or more steps in Q biosynthesis. COQ6 gene encodes a mitochondrial flavin-dependent monooxygenase required for coenzyme Q biosynthesis.

Organism species: Homo sapiens (Human)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Hu01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Hu01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Hu01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Hu01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Hu01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Organism species: Mus musculus (Mouse)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Mu01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Mu01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Mu01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Mu01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Mu01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Organism species: Rattus norvegicus (Rat)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Ra01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Ra01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Ra01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Ra01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Ra01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Organism species: Canis familiaris; Canine (Dog)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Ca01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Ca01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Ca01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Ca01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Ca01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Organism species: Sus scrofa; Porcine (Pig)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Po01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Po01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Po01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Po01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Po01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Organism species: Bos taurus; Bovine (Cattle)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Bo01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Bo01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Bo01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Bo01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Bo01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Organism species: Oryctolagus cuniculus (Rabbit)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Rb01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Rb01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Rb01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Rb01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Rb01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Organism species: Rhesus monkey (Simian)

PRODUCT TYPE CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPJ137Mo01 Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies MAJ137Mo01 Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IP.
PAJ137Mo01 Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6) WB; IHC; ICC; IF.
Assay Kits CLJ137Mo01 CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) CLIA assay for Antigen Detection
ELJ137Mo01 ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6) Enzyme-linked immunosorbent assay for Antigen Detection

Reference

"Identification of novel human genes evolutionarily conserved in Caenorhabditis elegans by comparative proteomics."
Genome Res. 10:703-713(2000) [PubMed] [Europe PMC] [Abstract]

"Complete sequencing and characterization of 21,243 full-length human cDNAs."
Nat. Genet. 36:40-45(2004) [PubMed] [Europe PMC] [Abstract]

"The DNA sequence and analysis of human chromosome 14."
Nature 421:601-607(2003) [PubMed] [Europe PMC] [Abstract]

"The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC)."
Genome Res. 14:2121-2127(2004) [PubMed] [Europe PMC] [Abstract]

"Initial characterization of the human central proteome."
BMC Syst. Biol. 5:17-17(2011) [PubMed] [Europe PMC] [Abstract]

"ADCK4 mutations promote steroid-resistant nephrotic syndrome through CoQ10 biosynthesis disruption."
J. Clin. Invest. 123:5179-5189(2013) [PubMed] [Europe PMC] [Abstract]

"COQ6 mutations in human patients produce nephrotic syndrome with sensorineural deafness."
J. Clin. Invest. 121:2013-2024(2011) [PubMed] [Europe PMC] [Abstract]