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Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CGI-10; Coenzyme Q10 monooxygenase 6; Ubiquinone biosynthesis monooxygenase COQ6, mitochondrial
Coenzyme Q (Q) is a lipid that functions as an electron carrier in the mitochondrial respiratory chain in eukaryotes. Coq6 mutants are unable to grow on nonfermentable carbon sources and do not synthesize Q but instead accumulate the Q biosynthetic intermediate 3-hexaprenyl-4-hydroxybenzoic acid. The Coq6 polypeptide is imported into the mitochondria in a membrane potential-dependent manner. Coq6p is a peripheral membrane protein that localizes to the matrix side of the inner mitochondrial membrane. COQ6 encodes a flavin-dependent monooxygenase required for one or more steps in Q biosynthesis. COQ6 gene encodes a mitochondrial flavin-dependent monooxygenase required for coenzyme Q biosynthesis.
Organism species: Homo sapiens (Human)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Hu01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Hu01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Hu01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Hu01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Hu01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Organism species: Mus musculus (Mouse)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Mu01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Mu01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Mu01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Mu01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Mu01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Organism species: Rattus norvegicus (Rat)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Ra01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Ra01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Ra01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Ra01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Ra01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Organism species: Canis familiaris; Canine (Dog)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Ca01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Ca01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Ca01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Ca01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Ca01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Organism species: Sus scrofa; Porcine (Pig)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Po01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Po01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Po01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Po01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Po01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Organism species: Bos taurus; Bovine (Cattle)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Bo01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Bo01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Bo01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Bo01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Bo01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Organism species: Oryctolagus cuniculus (Rabbit)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Rb01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Rb01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Rb01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Rb01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Rb01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Organism species: Rhesus monkey (Simian)
PRODUCT TYPE
CATALOG NO.
PRODUCT NAME
APPLICATIONS
Proteins
RPJ137Mo01
Recombinant Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies
MAJ137Mo01
Monoclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IP.
PAJ137Mo01
Polyclonal Antibody to Coenzyme Q6 Homolog, Monooxygenase (COQ6)
WB; IHC; ICC; IF.
Assay Kits
CLJ137Mo01
CLIA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
CLIA assay for Antigen Detection
ELJ137Mo01
ELISA Kit for Coenzyme Q6 Homolog, Monooxygenase (COQ6)
Enzyme-linked immunosorbent assay for Antigen Detection
Reference
"Identification of novel human genes evolutionarily conserved in Caenorhabditis elegans by comparative proteomics." Genome Res. 10:703-713(2000) [PubMed ] [Europe PMC ] [Abstract ]
"Complete sequencing and characterization of 21,243 full-length human cDNAs." Nat. Genet. 36:40-45(2004) [PubMed ] [Europe PMC ] [Abstract ]
"The DNA sequence and analysis of human chromosome 14." Nature 421:601-607(2003) [PubMed ] [Europe PMC ] [Abstract ]
"The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC)." Genome Res. 14:2121-2127(2004) [PubMed ] [Europe PMC ] [Abstract ]
"Initial characterization of the human central proteome." BMC Syst. Biol. 5:17-17(2011) [PubMed ] [Europe PMC ] [Abstract ]
"ADCK4 mutations promote steroid-resistant nephrotic syndrome through CoQ10 biosynthesis disruption." J. Clin. Invest. 123:5179-5189(2013) [PubMed ] [Europe PMC ] [Abstract ]
"COQ6 mutations in human patients produce nephrotic syndrome with sensorineural deafness." J. Clin. Invest. 121:2013-2024(2011) [PubMed ] [Europe PMC ] [Abstract ]